The progressive muscular dystrophy is primarily a disease of the striated musles of unknown etiology characterized by progressive degeneration and regeneration. Because of the nature of disease, management of patient requires specialized knowledge and skill.
This paper reports total 101 patients registered in the Muscular Dystrophy Association of Korea (4 females and 97 males). The results were obtained by questionnaire sent to patients. They are 52 Duchenne type, 3 Becker type, 27 Limb-girdle type, and 6 Facioscapulohumeral type muscular dystrophy.
The results of these studies were as follows;
1) Korean floor Ondol style classification(Kang´s method) for functional stage in the home bound patients is more practical than Swinyard, Price, Ueda method especially in questionnaire.
2) The familial genetic history reveals 30.7°o and the nonfamilial mutation history reveals 69.3°0.
3) The 76.9°0 of Duchenne type patients need special education program rather than ordinary school program.
4) The diagnostic criteria included history and physical examination, serum enzyme study, electromyography and muscle biopsy.
5) It seemed to be considered the factors related in our psycosocial background, parents counseling and active patients care should be focused effectively in Rehabilitation Program in the Rehabilitation institute.
6) For further investigation in the subject, Muscle Study Group is to be suggested. Muscular Dystrophy Association needs support by civilian as well as governmental base.
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